Primary Pulmonary Ewing's Sarcoma/Primitive NeuroectodermalTumor in a 67-year-old Man : Primary Pulmonary Ewing's Sarcoma/Primitive NeuroectodermalTumor in a 67-year-old Man
Primary Pulmonary Ewing's Sarcoma/Primitive NeuroectodermalTumor in a 67-year-old Man
- 주제(키워드) Sarcoma , Ewing’s , Neuroectodermal Tumors , Primitive , Peripheral , Lung
- 발행기관 대한의학회
- 발행년도 2007
- 총서유형 Journal
- UCI G704-000345.2007.22.S.027
- KCI ID ART001090080
- 본문언어 영어
초록/요약
Extraskeletal Ewing’s sarcoma (EES) is a branch of neuroectodermal tumor (PNET), which is very rare soft tissue sarcoma. We report a case of EES/PNET arising is the lung of a 67-yr-old man. Computed tomography, bone scintigraphy, and positron emission tomography confirmed the mass to have a primary pulmonary origin. The mass showed positive reactivity in the Periodic Acid Schiff (PAS) stain and MIC-2 immunoreactivity in immunohistochemical stain. Fluorescence in situ hybridization (FISH) was performed, which revealed an EWSR1 (Ewing sarcoma breakpoint region 1) 22q12 rearrangement. The diagnosis was confirmed both pathologically and genetically. The mass lesion was resected, and the patient is currently undergoing chemotherapy.
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